Idiopathic diffuse interstitial pulmonary fibrosis
Alternative names:
idiopathic pulmonary fibrosis
Treatment:
The objective of treatment is supportive therapy, as there are no curative treatments. Medications such as corticosteroids and cytotoxic drugs may be given to suppress the immune system.
Heart-lung and single lung transplantation may be indicated for highly selected patients with end-stage pulmonary fibrosis (a fibrotic lung disease).
Support groups:
The stress of illness can often be helped by joining a support group where members share common experiences and problems. See lung disease - support group.
Expectations (prognosis):
Up to 20% of patients improve with drug therapy, but the disease is progressive, with respiratory failure the eventual outcome. Average survival time is 4 years after the onset of symptoms.
Complications:
Calling your health care provider:
Call for an appointment with the health care provider if persistent cough, chest pain, and shortness of breath develop.
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