Sickle cell anemia
Alternative names:
anemia - sickle cell; Hemoglobin SS disease (Hb SS); Sickle
cell disease.
Prevention:
Sickle cell anemia can only result when two carriers with
sickle cell trait have a child together. Therefore, genetic
counseling is recommended for all carriers of sickle
cell trait (about 1 in 12 African Americans has sickle
cell trait). Prenatal diagnosis of sickle cell anemia is also
available. Prompt treatment of infections, adequate oxygenation,
and preventing dehydration may prevent sickling of red blood
cells. Antibiotics and vaccinations may prevent infections.
General health visits with a physician are recommended to
ensure the patients is getting adequate nutrition, maintaining
proper activity levels, and receiving proper vaccinations.
In incentive spirometry, the patient breathes into a plastic
tube that has a ball inside. By trying to breathe hard enough
to force the ball up the tube, the patient receives more oxygen.
Using this treatment when chest pains begin may decrease the
complications of acute chest syndrome. Prenatal diagnosis
is now possible for couples at risk of producing a child with
sickle cell anemia.
Updated Date: 05/08/00
Updated by: Bradley G. Somer, MD, Division
of Hematology-Oncology, Hospital University of Pennsylvania,
Verimed Health Network
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