Hemophilia B
Alternative names:
Christmas disease; factor IX hemophilia
Treatment:
Standard treatment is infusion of factor IX concentrates to replace the defective clotting factor. The amount infused depends upon the severity of bleeding, the site of the bleeding, and the size of the patient. Hepatitis B vaccine is recommended for individuals with Hemophilia B because they are at increased risk of developing hepatitis due to exposure to blood products.
To prevent a bleeding crisis, people with hemophilia and their families can be taught to administer factor IX concentrates at home at the first signs of bleeding. People with severe forms of the disease may need regular prophylactic infusions.
Depending on the severity of the disease, factor IX concentrate may be given prior to dental extractions and surgery to prevent bleeding.
Support groups:
The stress of illness can often be helped by joining a support group where members share common experiences and problems. See hemophilia - support group.
Expectations (prognosis):
The outcome is good with treatment; most people with hemophilia are able to lead relatively normal lives. A small percentage of people develop inhibitors of factor IX and may die from loss of blood.
Complications:
Calling your health care provider:
Call your health care provider if symptoms of a bleeding disorder develop.
Call for an appointment with your health care provider (for screening) if a family member has been diagnosed with hemophilia B.
Call for an appointment with your health care provider if you have hemophilia B and you plan to have children.
|
