Huntington disease

Alternative names:

Huntington chorea

Treatment:

There is no cure for Huntington disease, and there is no known way to stop progression of the disorder. Treatment is aimed at slowing progression and maximizing ability to function for as long as possible.

Medications vary depending on the symptoms. Dopamine blockers such as haloperidol or phenothiazine medications may reduce abnormal behaviors and movements. Reserpine and other medications have been used, with varying success.

Symptomatic treatment for the dementia is similar to that of any organic brain syndrome. Initially, reminders and aids may improve the ability to function. There is a progressive need for assistance and supervision, and 24-hour care may eventually be required.

Expectations (prognosis):

Huntington disease causes progressive disability. The disorder is usually fatal within 15 to 20 years. The cause of death is often infection, although suicide is also common.

Complications:

• loss of ability to care for self
• loss of ability to interact
• injuries to self or others
• increased risk of infections
• depression

Calling your health care provider:

Call your health care provider if symptoms of this disorder develop. Sudden change in mental status may indicate development of a different disorder.