Hirschsprung's disease

Alternative names:

congenital megacolon

Treatment:

Most cases require surgery. A temporary colostomy (an opening from the bowel to the abdominal wall) is performed as soon as possible to prevent complications associated with bowel obstruction. Resection (removal) of the affected bowel segment and reconnection of the colon is usually performed when the infant is 6 months or older. Supportive measures include rehydration with intravenous fluids and correction of electrolyte abnormalities if present. Antibiotic therapy is indicated if a hole in the bowel (perforation) or enterocolitis has occurred.

Expectations (prognosis):

Symptoms are eliminated in 90% of children after surgical treatment. A better outcome is associated with early treatment.

Complications:

• perforation of the intestine
• enterocolitis

Calling your health care provider:

Call your child's health care provider if symptoms of Hirschsprung's disease develop.

Call your child's health care provider if abdominal pain or other new symptoms develop after treatment for Hirschsprung's disease.