Agammaglobulinemia
Alternative names:
Bruton agammaglobulinemia; X-linked agammaglobulinemia
Treatment:
The goal of treatment is to reduce the number and severity of infections.
Intramuscular injections of immune serum globulin (gamma globulin injections) help to boost the immune system. Infusions of blood plasma into a vein gives a quick supplement to the immune system (plasma contains antibodies, including IgG, IgM, and IgA). High doses of high titer gammaglobulin are needed for severe infections.
Antibiotics are available for the treatment of bacterial infections.
Expectations (prognosis):
Treatment with immune globulins has improved the health of people with agammaglobulinemia. Without treatment, most severe infections are fatal.
Complications:
Calling your health care provider:
Call for an appointment with your health care provider if you or your child has experienced frequent infections.
Call for an appointment with your health care provider if you have a family history of agammaglobulinemia or other immunodeficiency disorder and you are planning to have children; ask the provider about genetic counseling.
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