Congenital Afibrinogenemia

Alternative names:

hypofibrinogenemia

Treatment:

Treatment is only necessary if there is severe bleeding or in preparation for surgery. Patients may be transfused with plasma (the liquid portion of the blood), concentrated fibrinogen, or cryoprecipitate (a blood product containing concentrated fibrinogen). Individuals with this condition should be immunized with the hepatitis B vaccine because of the increased risk of developing hepatitis due to transfusion of blood products.

Expectations (prognosis):

The prognosis is good when patients seek proper treatment.

Complications:

Complications usually only occur with trauma:

• bleeding from the umbilical cord
• bleeding from the mucous membranes
• gastrointestinal bleeding
• intracranial bleeding

Calling your health care provider:

Call your health care provider or seek emergency care if excessive bleeding occurs.

Notify your surgeon before you have surgery if you know or suspect you have a blood disorder.