Ectodermal dysplasia

Alternative names:

anhidrotic ectodermal dysplasia

Treatment:

There is no specific treatment for this disorder. Cosmetic and functional improvements can be made through the use of wigs in the absence of scalp hair and dentures to replace missing and defective teeth. Synthetic tears may be necessary to replace normal tearing and prevent drying of the eyes. The nose may have to be irrigated frequently to remove purulent debris and prevent infection. Temperature control is a constant problem. Affected people require a cooler climate and may require frequent cooling water baths or sprays to maintain a normal body temperature. (Water evaporating from the skin replaces the cooling function of sweat evaporating from the skin.)

Expectations (prognosis):

Ectodermal dysplasia is compatible with a normal life span, but constant attention must be paid to temperature regulation and other problems that may exist.

Complications:

• febrile seizures
• brain damage secondary to increased body temperature

Calling your health care provider:

Call for an appointment with your health care provider if your child shows symptoms of this disorder.