Incontinentia pigmenti syndrome

Alternative names:

Bloch-Sulzberger syndrome; IPS

Treatment:

There is no one treatment for IPS. Therapies must address the specific problems that are present.

Expectations (prognosis):

Prognosis varies depending on the degree of central nervous system involvement and visual impairment.

Complications:

• secondary infections of blistered skin
• mental retardation
• delayed development
• seizures
• paralysis
• muscle spasticity and difficulty walking
• visual problems

Calling your health care provider:

Call your health care provider if you have a family history of this disorder and are considering having children, or if your child shows symptoms that characterize this disorder.